Portal hypertension without known risk factors for hypertension, e.g., HEPATIC CIRRHOSIS and SCHISTOSOMIASIS. Idiopathic Noncirrhotic Portal Hypertension is most often associated with pathology in the PORTAL SYSTEM vasculature.
Also Known As:
Banti Disease; Banti Syndrome; Congestive Splenomegaly, Idiopathic; Disease, Banti's; Disease, Porto-Sinusoidal Vascular; Diseases, Porto-Sinusoidal Vascular; Fibrosis, Noncirrhotic Portal; Hypertension, Idiopathic Portal; Idiopathic Congestive Splenomegalies; Idiopathic Non Cirrhotic Portal Hypertension; Idiopathic Portal Hypertensions; Noncirrhotic Portal Fibroses; Portal Fibrosis, Noncirrhotic; Portal Hypertension, Idiopathic; Porto Sinusoidal Vascular Diseases; Porto-Sinusoidal Vascular Disease; Splenomegaly, Idiopathic Congestive; Syndrome, Banti's; Vascular Disease, Porto-Sinusoidal; Banti's Disease; Banti's Syndrome; INCPH; Idiopathic Congestive Splenomegaly; Idiopathic Non-Cirrhotic Portal Hypertension; Idiopathic Portal Hypertension; Noncirrhotic Portal Fibrosis; Porto-Sinusoidal Vascular Diseases