Portal Hypertensive Biliopathy as a Cause of Severe Cholestasis in Children With Congenital Hepatic Fibrosis.

Abstract

Portal hypertensive biliopathy may occur in patients with noncirrhotic hepatic fibrosis. Portal hypertensive biliopathy treatment should be focused on management of portal hypertension and relief of biliary obstruction. In patients with noncirrhotic portal fibrosis and symptomatic portal hypertensive biliopathy, portal decompression surgery by proximal splenorenal shunt is one successful treatment option.

• Authors: Aydın Dalgıç, Sinan Sarı, Mustafa Hakan Sözen, Neslihan Gürcan Kaya, Buket Dalgıç
• Journal: Experimental and clinical transplantation : official journal of the Middle East Society for Organ Transplantation (Exp Clin Transplant) Vol. 17 Issue Suppl 1 Pg. 223-225 (01 2019) ISSN: 2146-8427 [Electronic] Turkey
• PMID: 30777560 (Publication Type: Case Reports, Journal Article)

Topics

• Adolescent
• Biopsy
• Cholangiopancreatography, Magnetic Resonance
• Cholestasis (diagnosis, etiology, surgery)
• Endoscopy, Gastrointestinal
• Female
• Genetic Diseases, Inborn (complications, diagnosis)
• Humans
• Hypertension, Portal (diagnosis, etiology, surgery)
• Liver Cirrhosis (complications, diagnosis)
• Portasystemic Shunt, Surgical
• Severity of Illness Index
• Treatment Outcome