Autoimmune disease characterized by subepidermal blisters and linear deposition of autoantibodies at the dermoepidermal junction. The accumulated autoantibodies are of IMMUNOGLOBULIN A and occasionally IMMUNOGLOBULIN G classes against epidermal BASEMENT MEMBRANE proteins. The dermatosis is sometimes associated with malignancies and use of certain drugs (e.g., VANCOMYCIN).
Also Known As:
Chronic Bullous Disease of Childhood; Drug-induced Linear IgA Bullous Dermatosis; Drug-induced Linear IgA Dermatosis; Linear IgA Dermatosis; Linear IgA IgG Bullous Dermatosis; Linear IgA IgG Dermatosis; Dermatoses, Linear IgA; Dermatosis, Linear IgA; Drug induced Linear IgA Bullous Dermatosis; Drug induced Linear IgA Dermatosis; IgA Dermatoses, Linear; IgA Dermatosis, Linear; Linear IgA Dermatoses