Group of systemic vasculitis with a strong association with ANCA. The disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls.
Also Known As:
ANCA Associated Vasculitides; ANCA Associated Vasculitis; ANCA-Associated Vasculitide; Anti Neutrophil Cytoplasmic Antibody Associated Vasculitis; Pauci Immune Vasculitis; Pauci-Immune Vasculitides; Vasculitide, ANCA-Associated; Vasculitides, ANCA-Associated; Vasculitides, Pauci-Immune; Vasculitis, ANCA-Associated; Vasculitis, Pauci-Immune; ANCA-Associated Vasculitides; ANCA-Associated Vasculitis; Pauci-Immune Vasculitis