Group of hemorrhagic disorders in which the VON WILLEBRAND FACTOR is either quantitatively or qualitatively abnormal. They are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. Symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor VIII, and impaired platelet adhesion.
Also Known As:
von Willebrand's Disease; Vascular Pseudohemophilia; Von Willebrand Disorder; Von Willebrand's Factor Deficiency; von Willebrand Disease, Recessive Form; von Willebrand's Diseases; Angiohemophilias; Disorder, Von Willebrand; Pseudohemophilia, Vascular; Pseudohemophilias, Vascular; Vascular Hemophilia; Vascular Hemophilias; Vascular Pseudohemophilias; Angiohemophilia; Hemophilia, Vascular; von Willebrand Disease