Volatile anesthesia for a pediatric patient with very long-chain acyl-coenzyme A dehydrogenase deficiency: A case report.

Abstract

We report the case of a 3-year-old boy with very long-chain acyl-coenzyme A dehydrogenase deficiency presenting for adenotonsillectomy who was successfully and safely managed with a balanced anesthetic including sevoflurane. The anesthetic management is described, and the controversy surrounding volatile anesthetics in these patients is discussed.

• Authors: Aaron S Hess, Gregory M Rice, John D Jochman, Bridget L Muldowney
• Journal: Paediatric anaesthesia (Paediatr Anaesth) Vol. 28 Issue 3 Pg. 296-297 (03 2018) ISSN: 1460-9592 [Electronic] France
• PMID: 29316010 (Publication Type: Case Reports)
• Copyright: © 2018 John Wiley & Sons Ltd.

Chemical References

• Anesthetics, Inhalation
• Methyl Ethers
• Sevoflurane
• Acyl-CoA Dehydrogenase, Long-Chain

Topics

• Acyl-CoA Dehydrogenase, Long-Chain (deficiency)
• Adenoidectomy
• Anesthesia, Inhalation (methods)
• Anesthetics, Inhalation
• Child, Preschool
• Congenital Bone Marrow Failure Syndromes
• Humans
• Lipid Metabolism, Inborn Errors (complications)
• Male
• Methyl Ethers
• Mitochondrial Diseases (complications)
• Muscular Diseases (complications)
• Perioperative Care
• Premedication
• Sevoflurane
• Tonsillectomy