Congenital peribronchial myofibroblastic tumor: prenatal imaging clues to differentiate from other fetal chest lesions.

Abstract

We present a prenatal case of congenital peribronchial myofibroblastic tumor referred as a congenital pulmonary airway malformation (CPAM) with hydrops and polyhydramnios at 30 weeks' gestational age. US and fetal MRI findings did not fit with the referral diagnosis, raising the possibility of intrinsic lung tumor. Fetal hydrops worsened and the baby was successfully delivered by ex utero intrapartum treatment (EXIT) to resection at 31 weeks' gestational age. To the best of our knowledge, this is a unique case of congenital peribronchial myofibroblastic tumor that underwent comprehensive prenatal evaluation and EXIT procedure with good outcome.

• Authors: Maria A Calvo-Garcia, Foong-Yen Lim, Jerzy Stanek, Constance Bitters, Beth M Kline-Fath
• Journal: Pediatric radiology (Pediatr Radiol) Vol. 44 Issue 4 Pg. 479-83 (Apr 2014) ISSN: 1432-1998 [Electronic] Germany
• PMID: 24169903 (Publication Type: Case Reports, Journal Article)

Topics

• Diagnosis, Differential
• Female
• Fetal Diseases (diagnosis, surgery)
• Fibrosarcoma (congenital, diagnosis, surgery)
• Humans
• Infant, Newborn
• Lung Neoplasms (congenital, diagnosis, surgery)
• Magnetic Resonance Imaging
• Male
• Pregnancy
• Pregnancy Outcome
• Prenatal Diagnosis
• Ultrasonography, Prenatal
• Young Adult