Protrusion of abdominal structures into the THORAX as a result of embryologic defects in the DIAPHRAGM often present in the neonatal period. It can be isolated, syndromic, non-syndromic or be a part of chromosome abnormality. Associated pulmonary hypoplasia and PULMONARY HYPERTENSION can further complicate stabilization and surgical intervention.
Also Known As:
Hernias, Diaphragmatic, Congenital; Agenesis of Hemidiaphragm; Bochdalek Hernias; Congenital Diaphragmatic Defect; Morgagni Hernias; Morgagni's Hernias; Unilateral Agenesis of Diaphragm; Congenital Diaphragmatic Defects; Defect, Congenital Diaphragmatic; Defects, Congenital Diaphragmatic; Diaphragm Unilateral Ageneses; Diaphragm Unilateral Agenesis; Diaphragmatic Defect, Congenital; Diaphragmatic Defects, Congenital; Diaphragmatic Hernia, Congenital; Diaphragmatic Hernias, Congenital; Hemidiaphragm Ageneses; Hemidiaphragm Agenesis; Hernia, Bochdalek; Hernia, Congenital Diaphragmatic; Hernia, Morgagni; Hernia, Morgagni's; Hernias, Bochdalek; Hernias, Congenital Diaphragmatic; Hernias, Morgagni; Hernias, Morgagni's; Morgagnis Hernia; Morgagnis Hernias; Bochdalek Hernia; Congenital Diaphragmatic Hernia; Morgagni Hernia; Morgagni's Hernia