A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
Also Known As:
Familial Idiopathic Pulmonary Fibrosis; Fibrocystic Pulmonary Dysplasia; Fibrosing Alveolitis, Cryptogenic; Idiopathic Fibrosing Alveolitis, Chronic Form; Idiopathic Pulmonary Fibrosis, Familial; Interstitial Pneumonitis, Usual; Pulmonary Fibrosis, Idiopathic; Usual Interstitial Pneumonia; Cryptogenic Fibrosing Alveolitides; Dysplasia, Fibrocystic Pulmonary; Fibrocystic Pulmonary Dysplasias; Fibrosing Alveolitides, Cryptogenic; Idiopathic Pulmonary Fibroses; Interstitial Pneumonia, Usual; Pneumonitides, Usual Interstitial; Pneumonitis, Usual Interstitial; Pulmonary Dysplasia, Fibrocystic; Pulmonary Fibroses, Idiopathic; Usual Interstitial Pneumonias; Usual Interstitial Pneumonitides; Usual Interstitial Pneumonitis; Cryptogenic Fibrosing Alveolitis