An autosomal recessive disorder characterized by a triad of DEXTROCARDIA; INFERTILITY; and SINUSITIS. The syndrome is caused by mutations of DYNEIN genes encoding motility proteins which are components of sperm tails, and CILIA in the respiratory and the reproductive tracts.
Also Known As:
Kartagener's Syndrome; Syndrome, Kartagener; Syndrome, Kartagener's; Ciliary Dyskinesia, Primary, 1; Ciliary Dyskinesia, Primary, 1, With Or Without Situs Inversus; Dextrocardia, Bronchiectasis, and Sinusitis; Kartagener's Triad; Polynesian Bronchiectasis; Siewert Syndrome; Bronchiectasis, Polynesian; Kartageners Syndrome; Kartageners Triad; Polynesian Bronchiectases; Syndrome, Siewert; Kartagener Triad