Protein-losing enteropathy after Fontan operation for tricuspid atresia (imperforate tricuspid valve).

Abstract

Protein-losing enteropathy occurred in a 7-year-old girl with tricuspid atresia, concordant ventriculo-arterial connexions and a relatively large hypoplastic right ventricle, one year after an atrio-ventricular type of Fontan operation by means of a valveless woven Dacron conduit. Severe conduit regurgitation and a marked enlargement of the hypoplastic right ventricle were demonstrated at recatheterization. Insertion of a bioprosthetic valve at the base of the right atrial appendage led to a dramatic clinical recovery of the patient. The use of a valved conduit is recommended when an atrioventricular type of Fontan repair is planned in patients with tricuspid atresia, concordant ventriculo-arterial connexions and relatively large hypoplastic right ventricle.

• Authors: G Crupi, G Locatelli, R Tiraboschi, M Villani, M De Tommasi, L Parenzan
• Journal: The Thoracic and cardiovascular surgeon (Thorac Cardiovasc Surg) Vol. 28 Issue 5 Pg. 359-63 (Oct 1980) ISSN: 0171-6425 [Print] Germany
• PMID: 6161437 (Publication Type: Case Reports, Journal Article)

Topics

• Aortic Valve Insufficiency (etiology)
• Cardiomegaly (complications)
• Child
• Female
• Heart Septal Defects (complications, surgery)
• Heart Valve Prosthesis
• Heart Ventricles (diagnostic imaging, surgery)
• Humans
• Methods
• Postoperative Complications
• Protein-Losing Enteropathies (etiology)
• Radiography
• Tricuspid Valve (abnormalities, diagnostic imaging, surgery)