Abstract |
While typically considered a pulmonary disease, cystic fibrosis patients develop significant nutritional complications and comorbidities, especially those who are pancreatic insufficient. Clinicians must have a high suspicion for cystic fibrosis among patients with clinical symptoms of pancreatic insufficiency, and pancreatic enzymatic replacement therapy (PERT) must be urgently initiated. PERT presents a myriad of considerations for patients and their supporting dieticians and clinicians, including types of administration, therapy failures, and complications.
|
Authors | Peter N Freswick, Elizabeth K Reid, Maria R Mascarenhas |
Journal | Nutrients
(Nutrients)
Vol. 14
Issue 7
(Mar 23 2022)
ISSN: 2072-6643 [Electronic] Switzerland |
PMID | 35405954
(Publication Type: Journal Article, Review)
|
Topics |
- Cystic Fibrosis
(complications, drug therapy)
- Enzyme Replacement Therapy
- Exocrine Pancreatic Insufficiency
(complications, etiology)
- Humans
- Pancreas
- Pancreatic Diseases
(complications)
|