Progression of Central-peripheral Band and Traction Bronchiectasis Clusters Leading to Chronic Respiratory Failure in a Patient with Fibrotic Pulmonary Sarcoidosis.

Abstract

We herein report a rare case of pulmonary sarcoidosis leading to chronic respiratory failure with restrictive ventilatory impairment during a 53-year-long observation period. Nine years after the histological diagnosis of stage I sarcoidosis on chest X-ray in a woman in her 20s, she developed bilateral reticular and granular opacities on chest computed tomography and was started on prednisone for 18 years. Seven years after prednisone withdrawal, these persisting opacities around the bronchovascular bundle, including a central-peripheral band, had progressed, forming traction bronchiectasis clusters and peripheral cysts, some of which developed continuously at the distal side of these clusters, with eventual upper lobe shrinkage.

• Authors: Michiru Sawahata, Noriharu Shijubo, Takeshi Johkoh, Takeshi Kawanobe, Yasumaro Fujiki, Masashi Bando, Koichi Hagiwara, Tamiko Takemura, Satoshi Konno, Tetsuo Yamaguchi
• Journal: Internal medicine (Tokyo, Japan) (Intern Med) Vol. 60 Issue 1 Pg. 111-116 (Jan 01 2021) ISSN: 1349-7235 [Electronic] Japan
• PMID: 32830175 (Publication Type: Case Reports, Journal Article)

Topics

• Bronchiectasis (complications, diagnostic imaging)
• Female
• Humans
• Respiratory Insufficiency (etiology)
• Sarcoidosis
• Sarcoidosis, Pulmonary (diagnosis, diagnostic imaging)
• Traction