Ossifying fibromyxoid tumor of the trunk mimicking hydatid cyst: A case report.

Abstract

INTRODUCTION:

Ossifying fibromyxoid tumor (OFMT) is a rare lesion that generally occurs in the soft tissues of proximal limbs, head or neck and presents as a slowly growing mass. Abdominal or trunk locations are extremely rare.

PRESENTATION OF CASE:

We report a case of 50-year-old man who presented with a painless, slow growing epigastric mass for 5 years. Radiologic assessment revealed a well circumscribed median subcutaneous parietal mass lesion present in front of the xiphoid process suspicious of a calcified hydatid cyst. Diagnosis of OFMT was made on histopathological examination of the resected specimen.

DISCUSSION:

OFMT most often presents as a single swelling arising from the subcutaneous soft tissues or skeletal muscles of the extremities. Multifocal presentation is exceedingly rare. Radiologically, a peripheral shell of bone is seen in more than 50% cases. On MRI, myxofibrous stroma appears isointense to muscle on T1 and of intermediate to high signal intensity on T2. Surgical excision is the mainstay of treatment. Histologically, the tumor has a thick fibrous capsule with a complete or partial underlying layer of metaplastic woven or lamellar bone. Tumor is composed of uniform round, ovoid, or spindle-shaped cells arranged in nests and cords embedded in a variably myxoid and collagenous Alcian blue-positive stroma. On immunochemistry, the tumor cells are positive for S100 protein and desmin in 90% and 50% cases respectively.

CONCLUSION:

OFMT is a rare soft tissue tumor with malignant potential often misdiagnosed as a benign lesion. Complete surgical excision should be performed to prevent local recurrence.

• Authors: Nihed Abdessayed, Sarra Mestiri, Houssem Ammar, Ahlem Bdioui, Amine Chhaidar, Omar Toumi, Nozha Mhamdi, Rahul Gupta, Marwa Guerfela, Moncef Mokni
• Journal: International journal of surgery case reports (Int J Surg Case Rep) Vol. 39 Pg. 80-83 ( 2017) ISSN: 2210-2612 [Print] Netherlands
• PMID: 28822312 (Publication Type: Journal Article)
• Copyright: Copyright © 2017 The Authors. Published by Elsevier Ltd.. All rights reserved.