Fontan operation with bilateral conduits for the treatment of pulmonary arteriovenous fistulas in a patient with polysplenia after reconstruction of a non-confluent pulmonary artery.

Abstract

We describe a case involving a successful Fontan procedure for the treatment of pulmonary arteriovenous fistulas in a patient with polysplenia. The patient was diagnosed with bilateral superior vena cavae, interrupted inferior vena cava with azygos connection, wide separate hepatic veins, and central pulmonary artery stenosis following repair of a non-confluent pulmonary artery. Bilateral extracardiac conduits were used to connect each hepatic vein to the pulmonary artery, opposite each superior vena cava. Clinical improvement in the pulmonary arteriovenous fistulas was observed within 4 months after surgery.

• Authors: Yuji Tominaga, Hiroaki Kawata, Shigemitsu Iwai, Sanae Yamauchi
• Journal: Journal of cardiac surgery (J Card Surg) Vol. 32 Issue 6 Pg. 387-389 (Jun 2017) ISSN: 1540-8191 [Electronic] United States
• PMID: 28497477 (Publication Type: Case Reports, Journal Article)
• Copyright: © 2017 Wiley Periodicals, Inc.

Topics

• Arteriovenous Fistula (etiology, surgery)
• Child, Preschool
• Female
• Fontan Procedure (methods)
• Hepatic Veins (abnormalities, surgery)
• Heterotaxy Syndrome (complications)
• Humans
• Postoperative Complications (etiology)
• Pulmonary Artery (abnormalities, surgery)
• Pulmonary Veins (abnormalities)
• Plastic Surgery Procedures
• Stenosis, Pulmonary Artery (etiology)
• Time Factors
• Vascular Surgical Procedures
• Vena Cava, Inferior (abnormalities)
• Vena Cava, Superior (abnormalities)