High Le Fort I osteotomy for correction of mid-face deformity in Crouzon syndrome.

Abstract

An 18-year-old woman with mild Crouzon syndrome was referred with malocclusion and mandibular protrusion. Examination revealed Class III canine and molar relationships, hypoplastic maxilla, 1-mm overbite, and -2-mm overjet. Analysis showed 69° sella-nasion-A, 73.6° sella-nasion-B, and -4.6° A point-nasion-B point angles. Polysomnography revealed respiratory disturbance and 6.3% oxygen desaturation indices of 5.4/h and 9.0/h. We performed double-jaw surgery using high Le Fort I osteotomy and bilateral sagittal split ramus osteotomy for midfacial deformity correction. Twelve months post-surgery, her measures were 70.8°, 72°, -1.2°, 3.0/h, and 6.1/h, respectively. Esthetics were satisfactory. High Le Fort I osteotomy is effective for midfacial deformity correction in patients with Crouzon syndrome.

• Authors: Yasumichi Nakajima, Hiroyuki Nakano, Tomoki Sumida, Tomohiro Yamada, Kazuya Inoue, Goro Sugiyama, Katsuaki Mishima, Yoshihide Mori
• Journal: Congenital anomalies (Congenit Anom (Kyoto)) Vol. 56 Issue 5 Pg. 240-2 (Sep 2016) ISSN: 1741-4520 [Electronic] Australia
• PMID: 27092811 (Publication Type: Case Reports)
• Copyright: © 2016 Japanese Teratology Society.

Topics

• Adolescent
• Cephalometry
• Craniofacial Dysostosis (diagnosis, surgery)
• Female
• Humans
• Maxilla (abnormalities, surgery)
• Osteotomy, Le Fort (methods)
• Phenotype
• Tomography, X-Ray Computed
• Treatment Outcome