Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome).

Abstract

Frontometaphyseal dysplasia (FMD), also called Gorlin-Cohen syndrome, is a rare hereditary X-linked dominant craniotubular bone disorder. The presentation describes the airway management of a 2-year-old child suffering from FMD with significant retrognathia, posted for major long bone corrective osteotomy. Induction with a combination of dexmedetomidine and ketamine preceded a successful endotracheal intubation under spontaneous ventilation.

• Authors: Anuradha Ganigara, Madhavi Nishtala, Yabagodu Rama Vakoda Chandrika, Kunigal Ravishankar Chandrakala
• Journal: Journal of anaesthesiology, clinical pharmacology (J Anaesthesiol Clin Pharmacol) Vol. 30 Issue 2 Pg. 279-80 (Apr 2014) ISSN: 0970-9185 [Print] India
• PMID: 24803775 (Publication Type: Case Reports)