Abstract | BACKGROUND: METHODS: The quality of life of Apert (n = 8) and Crouzon (n = 12) syndrome patients was assessed using the World Health Organization Quality of Life-100 questionnaire. The Mann-Whitney test was used to compare the quality-of-life scores between Apert and Crouzon patients. Values were considered significant for a confidence interval of 95 percent (p < 0.05). RESULTS: Apert patients showed an overall higher (score > 60 percent) quality of life in most World Health Organization Quality of Life-100 facets (68 percent) and domains (83.33 percent), with significance (p < 0.05) in three facets (energy and fatigue, mobility, and environment in the home), compared with Crouzon patients. CONCLUSION: Contrary to the authors' initial hypothesis, both the highest-functioning Apert patients and the Crouzon patients presented a satisfactory quality of life, demonstrating that these syndromic patients had acquired the necessary repertoire to manage the adverse daily situations of their lives.
|
Authors | Cassio Eduardo Raposo-Amaral, José Garcia Junqueira Neto, Rafael Denadai, Cassio Menezes Raposo-Amaral, Cesar Augusto Raposo-Amaral |
Journal | Plastic and reconstructive surgery
(Plast Reconstr Surg)
Vol. 133
Issue 2
Pg. 182e-191e
(Feb 2014)
ISSN: 1529-4242 [Electronic] United States |
PMID | 24469189
(Publication Type: Comparative Study, Journal Article, Observational Study)
|
Topics |
- Acrocephalosyndactylia
(diagnosis, physiopathology)
- Adolescent
- Adult
- Child
- Craniofacial Dysostosis
(diagnosis, physiopathology)
- Diagnostic Self Evaluation
- Female
- Humans
- Male
- Phenotype
- Quality of Life
- Retrospective Studies
- Young Adult
|