Maxillary bone lesions in McCune-Albright syndrome: a case report.

Abstract

OBJECTIVES:

In this study, we report on the clinical maxillary manifestations of a patient affected by McCune-Albright syndrome and the implications for orthodontic therapy.

MATERIALS AND METHODS:

A male, 8-year-old patient was examined at the Department of Orthodontics of the University of L'Aquila for a problem of anterior open-bite. In the clinical examination, a small swelling of the left hemi-maxilla was seen in the area corresponding to the root apex of 16 and under the tooth buds of 14 and 15. In a panoramic radiograph, a radio-opaque area was detected in this zone. From the computer tomography examination, a bone lesion was identified.

RESULTS:

Identification of this bone lesion led to the clinical-instrumental diagnosis of McCune-Albright syndrome. This was then confirmed in the histological diagnosis.

CONCLUSIONS:

It is always useful to have diagnostic doubts about atypical clinical manifestations at the craniofacial level, as they are often local signs of a systemic syndrome. This is important for patient health, and also for orthodontic treatment planning.

• Authors: Michele Leopardi, Vincenzo Parziale, Domenico Ciavarella, Claudio Chimenti
• Journal: Progress in orthodontics (Prog Orthod) Vol. 12 Issue 1 Pg. 84-9 ( 2011) ISSN: 2196-1042 [Electronic] Germany
• PMID: 21515236 (Publication Type: Case Reports, Journal Article)
• Copyright: Copyright © 2010 Società Italiana di Ortodonzia SIDO. Published by Elsevier Srl. All rights reserved.

Topics

• Child
• Fibrous Dysplasia, Polyostotic (complications, pathology)
• Humans
• Male
• Maxillary Diseases (diagnostic imaging, etiology, surgery)
• Open Bite (etiology)
• Paranasal Sinus Diseases (diagnostic imaging, etiology)
• Tomography, X-Ray Computed