Rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by CONSUMPTION COAGULOPATHY; THROMBOCYTOPENIA; and HEMOLYTIC ANEMIA. It is often associated with infantile Kaposiform HEMANGIOENDOTHELIOMA and other vascular tumors such as tufted ANGIOMA.
Also Known As:
Hemangioma-Thrombocytopenia Syndrome; Hemangioma Thrombocytopenia Syndromes; Kasabach Merritt Phenomenon; Kasabach Merritt Syndrome; Phenomenon, Kasabach-Merritt; Syndrome, Hemangioma Thrombocytopenia; Syndrome, Kasabach-Merritt; Syndrome, Thrombocytopenia-Hemangioma; Syndromes, Hemangioma Thrombocytopenia; Syndromes, Thrombocytopenia-Hemangioma; Thrombocytopenia Hemangioma Syndrome; Thrombocytopenia-Hemangioma Syndromes; Hemangioma Thrombocytopenia Syndrome; Kasabach-Merritt Phenomenon; Thrombocytopenia-Hemangioma Syndrome