Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.
Also Known As:
Hamman Rich Syndrome; Hamman-Rich Disease; Acute Interstitial Pneumonias; Acute Interstitial Pneumonitides; Hamman Rich Disease; Interstitial Pneumonia, Acute; Interstitial Pneumonitis, Acute; Pneumonia, Acute Interstitial; Pneumonitis, Acute Interstitial; Acute Interstitial Pneumonia; Acute Interstitial Pneumonitis