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5N,6S- (N'- butyliminomethylidene)- 6- thio- 1- deoxygalactonojirimycin

a pharmacological chaperone for lysosomal beta-galactosidase; structure in first source
Also Known As:
6S-NBI-DGJ
Networked: 1 relevant articles (0 outcomes, 0 trials/studies)

Bio-Agent Context: Research Results

Experts

1. Aguilar-Moncayo, Matilde: 1 article (03/2013)
2. García Fernández, José M: 1 article (03/2013)
3. García-Moreno, M Isabel: 1 article (03/2013)
4. Higaki, Katsumi: 1 article (03/2013)
5. Hirano, Yuki: 1 article (03/2013)
6. Mena-Barragán, Teresa: 1 article (03/2013)
7. Nanba, Eiji: 1 article (03/2013)
8. Ninomiya, Haruaki: 1 article (03/2013)
9. Ohno, Kousaku: 1 article (03/2013)
10. Ortiz Mellet, Carmen: 1 article (03/2013)

Related Diseases

1. GM1 Gangliosidosis (Gangliosidosis GM1)

Related Therapies and Procedures

1. Oral Administration