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Short QT Syndrome 1

mutation in KCNH2

Networked: 2 relevant articles (0 outcomes, 0 trials/studies)

Disease Context: Research Results

Related Diseases

1.	Channelopathies
2.	Arrhythmogenic Right Ventricular Dysplasia (Arrhythmogenic Right Ventricular Cardiomyopathy)
3.	Brugada Syndrome 8
4.	Long Qt Syndrome 9
5.	Polymorphic catecholergic ventricular tachycardia

Experts

1.	Behrends, Jan C: 1 article (01/2019)
2.	Bode, Christoph: 1 article (01/2019)
3.	Bodi, Ilona: 1 article (01/2019)
4.	Brunner, Michael: 1 article (01/2019)
5.	Bugger, Heiko: 1 article (01/2019)
6.	Doleschall, Zoltan: 1 article (01/2019)
7.	Franke, Gerlind: 1 article (01/2019)
8.	Fürniss, Hannah: 1 article (01/2019)
9.	Jolivet, Genevieve: 1 article (01/2019)
10.	Lang, Corinna N: 1 article (01/2019)

Drugs and Biologics

Drugs and Important Biological Agents (IBA) related to Short QT Syndrome 1:

1.	Quinidine (Chinidin)FDA LinkGeneric 01/01/2019 - "Short-QT syndrome 1 rabbits mimic the human disease phenotype on all levels with shortened QT/APD and increased VT/VF-inducibility and show similar beneficial responses to quinidine, indicating their value for elucidation of arrhythmogenic mechanisms and identification of novel anti-arrhythmic strategies."
2.	Anti-Arrhythmia AgentsIBA 01/01/2019 - "Short-QT syndrome 1 rabbits mimic the human disease phenotype on all levels with shortened QT/APD and increased VT/VF-inducibility and show similar beneficial responses to quinidine, indicating their value for elucidation of arrhythmogenic mechanisms and identification of novel anti-arrhythmic strategies."

Therapies and Procedures

1.	Secondary Prevention 01/01/2016 - "In diagnosed channelopathy or arrhythmogenic right ventricular cardiomyopathy index cases, 44 patients received secondary prevention implantable cardioverter-defibrillators (long QT syndrome, 9; Brugada syndrome, 8; catecholaminergic polymorphic ventricular tachycardia, 3; short QT syndrome, 1; and arrhythmogenic right ventricular cardiomyopathy, 23). "
2.	Implantable Defibrillators (Implantable Cardioverter-Defibrillator) 01/01/2016 - "In diagnosed channelopathy or arrhythmogenic right ventricular cardiomyopathy index cases, 44 patients received secondary prevention implantable cardioverter-defibrillators (long QT syndrome, 9; Brugada syndrome, 8; catecholaminergic polymorphic ventricular tachycardia, 3; short QT syndrome, 1; and arrhythmogenic right ventricular cardiomyopathy, 23). "