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Pentalogy of Cantrell Summary

Description: Rare congenital deformity syndrome characterized by a combination of five anomalies as a result of neural tube defect. The five anomalies are a midline supraumbilical abdominal wall defect (e.g., OMPHALOCELE), a lower STERNUM defect, a congenital intracardiac defect, an anterior DIAPHRAGM defect, and a diaphragmatic PERICARDIUM defect (e.g., PERICARDIAL EFFUSION). Variants with incomplete and variable combinations of the defects are known. ECTOPIA CORDIS; CLEFT LIP; and CLEFT PALATE are often associated with the syndrome.

Also Known As: Cantrell's Pentalogy; Cantrells Pentalogy; Pentalogy, Cantrell; Pentalogy, Cantrell's; Thoracoabdominal Syndromes Show All >>

Networked: 27 relevant articles (0 outcomes, 0 trials/studies) for this Disease

Key Drugs and Agents for Pentalogy of Cantrell

Efficacy Chart >>
Drugs and Important Biological Agents (IBA) related to treatments:
  1. Sternal cleft : 4 results : IBA
  2. Carbon Monoxide : 2 results : IBA
  3. Omphalocele exstrophy imperforate anus : 2 results : IBA
  4. Ectrodactyly : 2 results : IBA
  5. Tretinoin (Retinoic Acid) : 1 result : FDA 27 Generic
  6. Retinaldehyde (Retinal) : 1 result : IBA
  7. Polyglycolic Acid (Polyglycolide) : 1 result : IBA
  8. Oxidoreductases : 1 result : IBA
  9. Glucose (Dextrose) : 1 result : FDA 175 Generic
  10. Frontonasal dysplasia : 1 result : IBA
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Diseases Related to Pentalogy of Cantrell

  1. Umbilical Hernia (Omphalocele)
  2. Ectopia Cordis
  3. Diaphragmatic Hernia
  4. Focal Dermal Hypoplasia (Syndrome, Goltz)
  5. Pentalogy of Cantrell
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Key Therapies for Pentalogy of Cantrell

Efficacy Chart >>
  1. Blalock-Taussig Procedure : 1 result
  2. Transplants (Transplant) : 1 result
  3. Stents : 1 result
  4. Postoperative Care : 1 result
  5. Pneumonectomy (Lung Volume Reduction) : 1 result
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