Search Login Register

Hereditary Coproporphyria (Coproporphyrinogen Oxidase Deficiency) Summary

Description: An autosomal dominant porphyria that is due to a deficiency of COPROPORPHYRINOGEN OXIDASE in the LIVER, the sixth enzyme in the 8-enzyme biosynthetic pathway of HEME. Clinical features include both neurological symptoms and cutaneous lesions. Patients excrete increased levels of porphyrin precursors, 5-AMINOLEVULINATE and COPROPORPHYRINS.

Also Known As: Coproporphyrinogen Oxidase Deficiency; Coproporphyria, Hereditary; Deficiency, Coproporphyrinogen Oxidase

Networked: 104 relevant articles (4 outcomes, 6 trials/studies) for this Disease

Key Drugs and Agents for Hereditary Coproporphyria

Efficacy Chart >>
Drugs and Important Biological Agents (IBA) related to treatments:
  1. Porphyrins : 1 outcome 2 studies in 15 results : IBA
  2. Ligases : 1 outcome in 2 results : IBA
  3. Hormones : 1 outcome in 1 result : IBA
  4. Erythromycin (Erycette) : 1 outcome in 1 result : FDA 66 Generic
  5. Coproporphyrinogen Oxidase (Coproporphyrinogen III Oxidases) : 1 study in 32 results : IBA
  6. Oxidoreductases : 1 study in 14 results : IBA
  7. Porphobilinogen : 1 study in 7 results : IBA
  8. Complementary DNA (cDNA) : 1 study in 3 results : IBA
  9. Riboflavin (Vitamin B2) : 1 study in 1 result : FDA 8 Generic
  10. coprogen : 1 study in 1 result : IBA
Show All >>

Diseases Related to Hereditary Coproporphyria

  1. Acute Intermittent Porphyria (Porphyria, Acute)
  2. Hepatic Porphyrias (Hepatic Porphyria)
  3. Erythropoietic Porphyria (Congenital Erythropoietic Porphyria)
  4. Porphyrias
  5. Porphyria Cutanea Tarda
Show All >>

Key Therapies for Hereditary Coproporphyria

Efficacy Chart >>
  1. Kidney Transplantation : 1 result
  2. Renal Dialysis (Hemodialysis) : 1 result
  3. Appendectomy : 1 result
  4. Epidural Anesthesia : 1 result
  5. Anesthesia : 1 result

CureHunter Inc. provides medical information and specifically does NOT provide medical advice.
© Copyright 2003-2016 CureHunter Inc., MeSH copyright NLM, Journal Articles copyright original owners.