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Familial Mediterranean Fever
(Periodic Disease)
Summary
Description:
A group of HEREDITARY AUTOINFLAMMATION DISEASES, characterized by recurrent fever, abdominal pain, headache, rash, PLEURISY; and ARTHRITIS. ORCHITIS; benign MENINGITIS; and AMYLOIDOSIS may also occur. Homozygous or compound heterozygous mutations in marenostrin gene result in autosomal recessive transmission; simple heterozygous, autosomal dominant form of the disease.
Also Known As:
Periodic Disease; Mediterranean Fever, Familial; Wolff Periodic Disease; Benign Paroxysmal Peritonitis; Familial Paroxysmal Polyserositis Show All >>
Networked: 1005
relevant articles (60 outcomes,
86 trials/studies)
for this Disease
Key Drugs and Agents for Familial Mediterranean Fever
Efficacy Chart >>
Drugs and Important Biological Agents (IBA) related to treatments:
-
Colchicine
:
42 outcomes 30 studies in 341 results
:
FDA 13
Generic
-
Interleukin 1 Receptor Antagonist Protein (Anakinra)
:
3 outcomes 3 studies in 18 results
:
FDA 2
-
Interferon-alpha (Interferon Alfa)
:
3 outcomes 2 studies in 8 results
:
FDA 2
-
canakinumab
:
3 outcomes in 5 results
:
FDA 2
-
rilonacept
:
2 outcomes 4 studies in 6 results
:
FDA 2
-
autosomal dominant familial Periodic fever
:
2 outcomes 2 studies in 77 results
: IBA
-
infliximab (Remicade)
:
2 outcomes 1 study in 9 results
:
FDA 2
-
Interleukin-1 (Interleukin 1)
:
2 outcomes in 16 results
: IBA
-
Amyloid (Amyloid Fibrils)
:
1 outcome 5 studies in 56 results
: IBA
-
C-Reactive Protein
:
1 outcome 3 studies in 9 results
: IBA
Show All >>
Diseases Related to Familial Mediterranean Fever
-
Amyloidosis
-
Familial Mediterranean Fever (Periodic Disease)
-
Pericarditis
-
Fever (Fevers)
-
Cryopyrin-Associated Periodic Syndromes
Show All >>
Key Therapies for Familial Mediterranean Fever
Efficacy Chart >>
-
Transplantation (Transplant Recipients)
:
1 outcome in 10 results
-
Bone Marrow Transplantation (Transplantation, Bone Marrow)
:
1 outcome in 4 results
-
Thyroidectomy
:
1 outcome in 1 result
-
Renal Dialysis (Hemodialysis)
:
1 study in 5 results
-
Hip Replacement Arthroplasty (Total Hip Replacement)
:
1 study in 2 results
Show All >>
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