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Hereditary Hyperbilirubinemia (Rotor Syndrome) Summary

Description: Inborn errors of bilirubin metabolism resulting in excessive amounts of bilirubin in the circulating blood, either because of increased bilirubin production or because of delayed clearance of bilirubin from the blood.

Also Known As: Rotor Syndrome; Syndrome, Rotor; Hyperbilirubinemia, Hereditary; Hyperbilirubinemia, Rotor Type; Hereditary Hyperbilirubinemias; Hyperbilirubinemias, Hereditary; Rotor Type Hyperbilirubinemia

Networked: 22 relevant articles (2 outcomes, 0 trials/studies) for this Disease

Key Drugs and Agents for Hereditary Hyperbilirubinemia

Efficacy Chart >>
Drugs and Important Biological Agents (IBA) related to treatments:
  1. Technetium Tc 99m Lidofenin : 1 outcome in 2 results : IBA
  2. diisopropylamine dichloroacetate (DIPA) : 1 outcome in 1 result : IBA
  3. Bilirubin : 10 results : IBA
  4. Peptides : 3 results : IBA
  5. Glutathione (Reduced Glutathione) : 3 results : IBA
  6. bilirubin glucuronate : 2 results : IBA
  7. Glutathione Disulfide (GSSG) : 1 result : FDA 3 Generic
  8. Ursodeoxycholic Acid (Urso) : 1 result : FDA 9 Generic
  9. Sulfobromophthalein (Sulfobromophthalein Sodium) : 1 result : IBA
  10. Retinaldehyde (Retinal) : 1 result : IBA
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Diseases Related to Hereditary Hyperbilirubinemia

  1. Chronic Idiopathic Jaundice (Dubin Johnson Syndrome)
  2. Hyperbilirubinemia
  3. Gilbert Disease
  4. Crigler-Najjar Syndrome (Syndrome, Crigler-Najjar)
  5. Stroke (Strokes)
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Key Therapies for Hereditary Hyperbilirubinemia

Efficacy Chart >>
  1. Oral Administration : 1 result

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