Simultaneous bilateral pallidoansotomy for idiopathic dystonia musculorum deformans.

Abstract

A 17-year-old Russian male with a 9-year diagnosed history of dystonia musculorum deformans manifested as severe tortipelvis, lordosis, and axial and appendicular spastic dystonia, refractory to medical therapy, is reported. This patient underwent a simultaneous bilateral pallidoansotomy with dramatic results. Postoperative evaluation revealed sustained alleviation of all dystonic symptoms and abnormal movements. Rapid recovery of useful strength in all limbs as well as dramatic improvement in coordination occurred. Bilateral posteroventral pallidotomy and pallidoansotomy in the past have proven effective in alleviation of all parkinsonian symptoms, including dyskinesia and dystonia, without the concurrent risk of intransigent side effects associated with bilateral thalamotomy or other stereotactic surgical procedures. Pallidoansotomy may prove to be the treatment of choice for idiopathic torsion dystonia and merits further investigation.

• Authors: R P Iacono, S M Kuniyoshi, R R Lonser, G Maeda, A M Inae, S Ashwal
• Journal: Pediatric neurology (Pediatr Neurol) Vol. 14 Issue 2 Pg. 145-8 (Feb 1996) ISSN: 0887-8994 [Print] United States
• PMID: 8703227 (Publication Type: Case Reports, Comparative Study, Journal Article)

Topics

• Adolescent
• Dystonia Musculorum Deformans (diagnosis, etiology, surgery)
• Functional Laterality
• Globus Pallidus (pathology, surgery)
• Humans
• Magnetic Resonance Imaging
• Male