Surgical experience of intracerebral
hematoma in an 8-month-old boy with severe
hemophilia B, which was not diagnosed preoperatively, was presented. Carotid angiography and removal of
hematoma by
craniotomy were carried out quite safely under fresh-
blood-transfusion. After several months
ventriculoperitoneal shunt was placed, because of progressing
hydrocephalus and multiple
porencephaly, this time, under the cover of the
factor IX complex. The clinical features of the
intracranial hemorrhage in
hemophilia were discussed, with analysis of 52 operation cases. Whenever we encounter a patient with
intracranial hemorrhage, especially in infancy, hemorrhagic diseases, as
hemophilia, must always be borne in mind. Although
intracranial hemorrhage is still the most fatal complication of
hemophilia, the surgical risk has been greatly diminished by advanced replacement
therapy. We stress the need of immediate diagnosis and positive surgical treatment with adequate replacement
therapy, if indicated.