Abstract |
We have treated by palliative or corrective surgery 12 patients with the complex cardiovascular anomalies associated with right isomerism ( asplenia syndrome) or left isomerism ( polysplenia syndrome). A systemic-pulmonary artery shunt was performed in 4 patients, with 2 early deaths. Anatomical intracardiac repair was successfully done in 2 patients, while an orthoterminal repair using a modified Fontan procedure was attempted in 5 patients, only 1 of whom survived. A 1-year-old girl with diffuse pulmonary arteriovenous fistulas associated with left isomerism was not considered a good candidate for operation after an exploratory sternotomy. The surgical options and technical problems related to the complex intracardiac morphology of these developmental syndromes are presented.
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Authors | C Marcelletti, R Di Donato, A Nijveld, C Squitieri, A H Bulterijs, M Naeff, J Schuller, A E Becker |
Journal | The Annals of thoracic surgery
(Ann Thorac Surg)
Vol. 35
Issue 4
Pg. 400-5
(Apr 1983)
ISSN: 0003-4975 [Print] Netherlands |
PMID | 6188418
(Publication Type: Journal Article)
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Topics |
- Adolescent
- Adult
- Arteriovenous Shunt, Surgical
- Child
- Child, Preschool
- Dextrocardia
(surgery)
- Female
- Heart Defects, Congenital
(surgery)
- Heart Septal Defects
(surgery)
- Humans
- Infant
- Infant, Newborn
- Male
- Palliative Care
- Prognosis
- Pulmonary Veins
(abnormalities)
- Spleen
(abnormalities)
- Syndrome
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