Abstract |
In a patient with Refsum's disease successful dietary control of the disease has been shown to depend on adequate energy and protein intake from phytanic acid-free sources and restriction of dietary phytanic acid to a maximum of 10 mg per day, with the provision of a generous amount of the essential fatty acid, linoleic acid. The present work gives data on the phytanic-acid content of various foodstuffs and suggests dietary manipulation of the patient. Although the role that chlorophyll-bound phytol plays in Refsum's disease is uncertain, it is advisable that this is eliminated until its role is more clearly identified.
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Authors | A Masters-Thomas, J Bailes, J D Billimoria, M E Clemens, F B Gibberd, N G Page |
Journal | Journal of human nutrition
(J Hum Nutr)
Vol. 34
Issue 4
Pg. 245-50
(Aug 1980)
ISSN: 0308-4329 [Print] England |
PMID | 6157716
(Publication Type: Case Reports, Journal Article)
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Chemical References |
- Dietary Proteins
- Linoleic Acids
- Phytanic Acid
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Topics |
- Adipose Tissue
(analysis)
- Adult
- Diet
- Dietary Proteins
(administration & dosage)
- Humans
- Linoleic Acids
- Male
- Phytanic Acid
(administration & dosage, blood)
- Refsum Disease
(blood, diet therapy)
- Retinitis Pigmentosa
(etiology)
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