Perioperative management of a patient with haemophilia B and PSVT undergoing radiofrequency ablation: A case report.

Abstract

Haemophilia B is a rare inherited bleeding disorder in which patients have impaired coagulation. This study describes a patient with Haemophilia B and paroxysmal supraventricular tachycardia (PSVT) who underwent radio frequency catheter ablation (RFCA). The perioperative replacement therapy with coagulation factor IX (FIX) was agreed upon after an interdisciplinary consultation involving a team of specialists in haematology, cardiovascular medicine and cardiothoracic surgery. There were no obvious bleeding points or complications during the perioperative period following the treatment, nor recurrence of PSVT within a three-year follow-up period. In summary, RFCA can be performed safely in patients with haemophilia B on the premise of developing an individualized perioperative exogenous coagulation factor supplementation regimen based upon an adequate preoperative evaluation and clinical monitoring and management by an interdisciplinary team.

• Authors: Yu Gan, Liping Ma, Pihua Fang
• Journal: The Journal of international medical research (J Int Med Res) Vol. 51 Issue 10 Pg. 3000605231208599 (Oct 2023) ISSN: 1473-2300 [Electronic] England
• PMID: 37890144 (Publication Type: Case Reports, Journal Article)

Topics

• Humans
• Tachycardia, Supraventricular (surgery)
• Hemophilia B (complications, surgery)
• Tachycardia, Paroxysmal
• Catheter Ablation
• Tachycardia, Ventricular (surgery)