Anesthetic considerations in the perioperative management of the patient with Jarcho-Levin Syndrome.

Abstract

Jarcho-Levin syndrome is an eponym used to describe a spectrum of small thoracic skeletal dysplasias with variable involvement of vertebrae and ribs. Initially considered lethal, it is currently compatible with life in its mildest forms. Bone alterations that lead to a restrictive respiratory pattern, recurrent respiratory infections and particular phenotype, can make perioperative anesthetic management difficult. The proper assessment of the airway is of special interest because it presents predictors of a difficult airway, as well as the prevention, early diagnosis and adequate treatment of respiratory failure. We present the case of a patient with Jarcho-Levin Syndrome who underwent vertebral distraction surgery, with its most notable implications in anesthetic management.

• Authors: F Rico Rodríguez, D A Camargo Espitia, A Mayoral Márquez, S Ruan Lin, M C Martín Lorenzo
• Journal: Revista espanola de anestesiologia y reanimacion (Rev Esp Anestesiol Reanim (Engl Ed)) (Sep 06 2023) ISSN: 2341-1929 [Electronic] Spain
• PMID: 37678455 (Publication Type: Case Reports)
• Copyright: Copyright © 2023 Sociedad Española de Anestesiología, Reanimación y Terapéutica del Dolor. Publicado por Elsevier España, S.L.U. All rights reserved.