Oral Care in Kindler Syndrome: 7-Year Follow-up of 2 Brothers.

Abstract

BACKGROUND:

Kindler poikiloderma is an inherited autosomal genodermatosis characterized by blistering of the epidermis and mucosae. Its prevalence is unknown.

CASE REPORT:

We monitored two brothers suffering from this pathology. Oral manifestations mainly take the form of periodontal lesions. In our patients we noted gingivitis progressing to periodontitis as follow-up care was not effective. We also diagnosed enamel hypoplasia, described more rarely in this pathology.

CONCLUSION:

Periodontitis in Kindler Syndrome responds to maintenance therapy, but the absence of surveillance is penalized by a deterioration in periodontal condition and complication of management. All restorative, endodontic, surgical, periodontal and orthodontic treatments should be performed with appropriate precautions.

• Authors: Isabelle Blanchet, Corinne Tardieu, Estelle Casazza
• Journal: The Journal of clinical pediatric dentistry (J Clin Pediatr Dent) Vol. 45 Issue 1 Pg. 41-47 (Jan 01 2021) ISSN: 1053-4628 [Print] United States
• PMID: 33690828 (Publication Type: Case Reports, Journal Article)

Topics

• Blister
• Epidermolysis Bullosa
• Follow-Up Studies
• Humans
• Male
• Periodontal Diseases (complications)
• Photosensitivity Disorders
• Siblings