Airway management in Nager Syndrome.

Abstract

Nager acrofacial dysostosis is a rare congenital syndrome characterized by malformed mandibulofacial structures and pre-axial upper limbs. Trismus and glossoptosis from mandibular abnormalities predisposes infants to life-threatening respiratory distress. A case of a Nager Syndrome mother delivering a similarly afflicted fetus is presented, with approaches to maintaining both tenuous airways described. Distinguishing this condition from similar syndromes is critical for care and prognosis.

• Authors: Allen S Ho, Pedram Aleshi, Sheila E Cohen, Peter J Koltai, Alan G Cheng
• Journal: International journal of pediatric otorhinolaryngology (Int J Pediatr Otorhinolaryngol) Vol. 72 Issue 12 Pg. 1885-8 (Dec 2008) ISSN: 0165-5876 [Print] Ireland
• PMID: 18947886 (Publication Type: Case Reports, Journal Article)

Topics

• Adult
• Female
• Humans
• Infant, Newborn
• Mandibulofacial Dysostosis (complications)
• Respiratory Distress Syndrome, Newborn (etiology, therapy)
• Syndrome
• Tracheotomy