An enzyme that specifically cleaves the ester sulfate of iduronic acid. Its deficiency has been demonstrated in Hunter's syndrome, which is characterized by an excess of dermatan sulfate and heparan sulfate. EC 3.1.6.13.
Also Known As:
Iduronate Sulfate Sulfatase; Corrective Factor, Hunter; Factor, Hunter Corrective; Sulfatase, Iduronate; Sulfatase, Iduronate Sulfate; Sulfatase, Sulfoiduronate; Sulfate Sulfatase, Iduronate; Sulfohydrolase, Iduronatesulfate; Hunter Corrective Factor; Iduronatesulfate Sulfohydrolase; Sulfoiduronate Sulfatase; L-Iduronate-2-sulfate 2-sulfohydrolase