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Lysine Malabsorption Syndrome
Networked:
1
relevant articles (
0
outcomes,
0
trials/studies)
Disease Context: Research Results
Congenital, Hereditary, and Neonatal Diseases and Abnormalities: 933
Inborn Genetic Diseases: 11939
Inborn Errors Metabolism: 1162
Inborn Errors Amino Acid Metabolism: 1
Lysine Malabsorption Syndrome: 1
Nutritional and Metabolic Diseases: 15
Metabolic Diseases: 10142
Inborn Errors Metabolism: 1162
Inborn Errors Amino Acid Metabolism: 1
Lysine Malabsorption Syndrome: 1
Malabsorption Syndromes: 639
Lysine Malabsorption Syndrome: 1
Amino Acids, Peptides, and Proteins: 1
Amino Acids: 30675
Essential Amino Acids: 1152
Lysine: 6737
Lysine Malabsorption Syndrome: 1
Basic Amino Acids: 178
Lysine: 6737
Lysine Malabsorption Syndrome: 1
Diamino Amino Acids: 101
Lysine: 6737
Lysine Malabsorption Syndrome: 1
Digestive System Diseases: 1042
Gastrointestinal Diseases: 5874
Intestinal Diseases: 1601
Malabsorption Syndromes: 639
Lysine Malabsorption Syndrome: 1
Related Diseases
1.
Hyperammonemia
2.
Hartnup Disease
3.
Cystinuria
4.
Cystinosis
5.
Lysinuric Protein Intolerance
Drugs and Biologics
Drugs and Important Biological Agents (IBA) related to Lysine Malabsorption Syndrome:
1.
Iminoglycinuria
IBA
07/01/1992 - "
The disorders were categorized into three types of transport defects, namely, brush-border membrane of epithelial cells of small intestine and kidney tubules (Hartnup disease, blue diaper syndrome, cystinuria, iminoglycinuria and lysine malabsorption syndrome), basolateral membrane (lysinuric protein intolerance) and membrane of intracellular organelles (cystinosis and hyperornitinemia-hyperammonemia-homocitrullinuria syndrome).
"